Summary
Epithelioid sarcoma, first described by Enzinger in 1970,
1
classically presents in young adults and usually arises in the distal extremities.
The proximal-type variant, first described in 1997 as a rare aggressive form of sarcoma,
usually arises more proximally.
2
It carries a higher mortality rate than classical limb epithelioid sarcoma and is
often resistant to multimodal treatment.
3
We report the case of a 27-year old male who had a delayed diagnosis of proximal-type
epithelioid sarcoma of the forearm. This was originally thought to be a necrotising
soft tissue infection and was unfortunately metastatic at the time of eventual diagnosis.
The clinical and histopathological features of this challenging tumour are discussed
and the relevant literature is reviewed.Keywords
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References
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- Proximal-type epithelioid sarcoma in the groin presenting as a diagnostic dilemma.Pathol Oncol Res. 2010;Jun; 16: 181-188
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Article info
Publication history
Published online: January 13, 2012
Accepted:
November 26,
2011
Received:
July 19,
2011
Identification
Copyright
© 2011 British Association of Plastic, Reconstructive and Aesthetic Surgeons. Published by Elsevier Inc. All rights reserved.
