Summary
Desmoid fibromatosis (also known as infantile or aggressive fibromatosis) is a rare
soft tissue tumour that is occasionally seen in children. Although histologically
benign, its growth pattern is highly aggressive often showing invasion of surrounding
musculature and bone.
Frequently found in cosmetically sensitive areas, complete excision can present a
challenging problem. However, incomplete surgical excision is associated with high
recurrence rates and although the disease responds to chemo and radiotherapy, both
carry significant risks in young children.
The management of four paediatric desmoid fibromatoses occurring in the midface is
discussed. The recent and pertinent literature is comprehensively reviewed and an
algorithm for the management of paediatric desmoid fibromatoses is proposed.
Keywords
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Article info
Publication history
Published online: December 12, 2011
Accepted:
September 15,
2011
Received:
May 18,
2011
Footnotes
☆This work has not been presented wholly or in part at any meeting.
Identification
Copyright
© 2011 British Association of Plastic, Reconstructive and Aesthetic Surgeons. Published by Elsevier Inc. All rights reserved.