Summary
Extra-skeletal Ewing's sarcoma (EES) is an uncommon malignancy, especially in the
head and neck region that may arise in various extra-osseous tissues. We report a
22-year-old male with an EES of the submandibular gland, which to the best of our
knowledge, has not been described previously. The patient who underwent combined treatment
with surgical resection and chemo-irradiation was disease free for 22 months but succumbed
to multi-organ metastases 14 months later. This case highlights the combined diagnostic
role of immunohistochemical, cytogenetic and radiological evaluation of EES. EES is
an aggressive cancer that requires multidisciplinary management with wide surgical
excision and adjunctive chemo-irradiation for the best outcome.
Keywords
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Article info
Publication history
Published online: June 15, 2006
Accepted:
January 1,
2006
Received:
October 6,
2005
Identification
Copyright
© 2006 British Association of Plastic, Reconstructive and Aesthetic Surgeons. Published by Elsevier Inc. All rights reserved.
