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Case report| Volume 60, ISSUE 3, P320-323, March 2007

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Collagenosis Nuchae: a case report of a rare and often misdiagnosed condition

  • A. Karonidis
    Correspondence
    Corresponding author. Sifnou 33, Agia Paraskevi, Athens 15343, Greece. Tel: +44 0 7974 427961 (mobile), +30 210 6007948 (home); fax: +30 210 6007948.
    Affiliations
    Department of Plastic and Reconstructive Surgery, Frenchay Hospital, North Bristol NHS Trust, Frenchay Park Road, Bristol BS16 1LE, UK
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  • H.S. Rigby
    Affiliations
    Department of Histopathology, Frenchay Hospital, North Bristol NHS Trust, Frenchay Park Road, Bristol BS16 1LE, UK
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  • A. Orlando
    Affiliations
    Department of Plastic and Reconstructive Surgery, Frenchay Hospital, North Bristol NHS Trust, Frenchay Park Road, Bristol BS16 1LE, UK
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      Summary

      Enzinger and Weiss first described Collagenosis Nuchae (CN) or nuchal fibroma (NF) in 1988. CN is a rare benign soft tissue tumour that arises from the posterior cervical subcutaneous tissue with predilection for the interscapular and paraspinal regions. It is more common in males. CN has been reported in association with trauma, diabetes, scleredema and Gardner's syndrome. The true incidence of CN is probably higher than recognised and CN should be in the differential diagnosis of head and neck lesions. Histological examination is required for the diagnosis. Careful total excision provides cure and accurate diagnosis. The purpose of this study is to review the epidemiological, clinical, histopathological and radiological features of this rare lesion, which is often misdiagnosed.

      Keywords

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