Summary
We report on a 16-year-old boy with Noonan syndrome who had short stature, hypertelorism,
mild hearing loss, webbed neck, pectus deformities, hypertrophic cardiomyopathy, low
posterior hairline, redundant skin, café au lait spot, curled hairs, foetal pads,
and undescended testes. The father and a sister of the boy were also found with mild
webbed neck, being possibly mildly affected individuals. The significant webbed-neck
deformity of the boy was completely corrected by subcutaneous resection of the proximal
half of the hypertrophic fascia bands, through small incisions hidden within the hairline.
The advantage of this procedure is simple, safe and effective, with no visible scar
on the surface of the neck.
Keywords
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References
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Article info
Publication history
Published online: June 02, 2006
Accepted:
February 4,
2006
Received:
January 21,
2006
Identification
Copyright
© 2006 The British Association of Plastic Surgeons. Published by Elsevier Inc. All rights reserved.
