Summary
Solitary and multicentric myofibromas are rare fibrous tumours with marked predilection
for infants and young children. Presentation is mainly before the age of 2 and lesions
are often congenital. Behaviour is usually benign, but mortality has been described
in lesions with visceral involvement.
We report a unique case of congenital solitary cutaneous infantile myofibroma in a
neonate associated with self-limiting thrombocytopaenia.
It is important to distinguish accurately these lesions from benign vascular tumours
like haemangiomas, locally aggressive vascular tumours like Kaposiform haemangioendotheliomas,
which are often associated with Kasabach–Merritt phenomenon and also with malignant
soft tissue tumours of infancy.
Keywords
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References
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Article info
Publication history
Published online: May 24, 2006
Accepted:
January 13,
2006
Received:
April 5,
2005
Identification
Copyright
© 2006 British Association of Plastic, Reconstructive and Aesthetic Surgeons. Published by Elsevier Inc. All rights reserved.
