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Summary
Cutis laxa is a genetically determined disorder of connective tissue, which is characterised by extreme cutaneous laxity. Cardio-respiratory involvement is sometimes a feature, and death may occur from these complications.
The clinical features and operative treatment of an affected girl are described, to illustrate the important part that plastic surgery can play in the management of the disorder.
The skin is not unduly fragile, excess bleeding does not occur, and incisions heal well. The instant results of cosmetic surgery are usually very good, but repeated operations may be necessary.
References
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Copyright
© 1970 E. & S. Livingstone. Published by Elsevier Inc.