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Summary
Basal encephalocoeles are rarely reported anomalies. Eight cases seen by one unit manifested external facial features and internal cerebral anomalies characteristic of the individual encephalocoele subgroups. CT and MR imaging delineates the anatomy of the skeletal defect and the associated cerebral abnormalities. Such imaging of cases of median cleft face syndrome may identify previously unsuspected basal encephalocoeles.
Transcranial correction with increased exposure, if needed, by the technique of facial bipartition has been performed in five cases.
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Article info
Publication history
Accepted:
April 16,
1993
Received:
January 12,
1993
Identification
Copyright
© 1993 The British Association of Plastic Surgeons. Published by Elsevier Inc.