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Research Article| Volume 46, ISSUE 6, P497-502, 1993

Basal encephalocoele: imaging and exposing the hernia

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      Summary

      Basal encephalocoeles are rarely reported anomalies. Eight cases seen by one unit manifested external facial features and internal cerebral anomalies characteristic of the individual encephalocoele subgroups. CT and MR imaging delineates the anatomy of the skeletal defect and the associated cerebral abnormalities. Such imaging of cases of median cleft face syndrome may identify previously unsuspected basal encephalocoeles.
      Transcranial correction with increased exposure, if needed, by the technique of facial bipartition has been performed in five cases.

      References

        • Gisselson L
        Intranasal forms of encephalomeningocele.
        Acta Octolaryngol. 1947; 35: 519-531
        • Yokota A
        • Matsukado Y
        • Fuwa I
        • Moroki K
        • Nagahiro S
        Anterior basal encephalocele of the neonatal and infantile period.
        Neurosurgery. 1986; 19: 968-978
        • Naidich TP
        • Osborn RE
        • Bauer B
        • Naidich MJ
        Median cleft face syndrome: MR and CT data from 11 children.
        Journal of Comp Assisted Tomog. 1988; 12: 57-64
        • Grubben C
        • Fryns JP
        • De Zegher F
        • Van den Berghe H
        Anterior basal encephalocele in the median cleft face syndrome. Comments on nosology and treatment.
        Genetic Counselling. 1990; 1: 103-109
        • Temple IK
        • Brunner H
        • Jones B
        • Burn J
        • Baraitser M
        Midline facial defects with ocular colobomata.
        Amer J Med Genet. 1990; 37: 23-27
        • Soyer P
        • Dobbelaere P
        • Benoit S
        Transalar sphenoidal encephalocele.
        Clin Radiology. 1991; 43: 65-67
        • Elster AD
        • Branch CL
        Transalar sphenoidal encephaloceles: a review of clinical and roentgen features in 8 cases.
        Radiology. 1989; 170: 245-247
        • Pollock J
        • Newton TH
        • Hoyt WF
        Transsphenoidal and transethmoidal encephaloceles: a review of clinical and roentgen features in 8 cases.
        Radiology. 1968; 90: 442-453
        • Barkovich A
        Anomalies of the corpus callosum: correlation with further anomalies of the brain.
        Amer J Roentgenology. 1988; 151: 171-179
        • Fenger C
        Basal hernias of the brain.
        Amer J Med Science. 1895; 109: 519-531
        • Lumsden A
        • Wilson JA
        • McLaren K
        • Maran AG
        Unusual polypoidal tumours of the nasal cavity: a clinicopathological review of 18 cases.
        Clin Otolaryngol. 1986; 11: 31-36
        • Chen J
        Antra-choanal polyp: a 10 year retrospective study in the pediatric population with a review of the literature.
        J Otolaryngol. 1989; 18: 168-172
        • Albernaz MS
        Intrasphenoidal encephalocele.
        Otolaryngol-Head and Neck Surg. 1991; 104: 279-281
        • De Myer W
        The median cleft face syndrome.
        Neurology. 1967; 17: 961-971
        • Lieblich JM
        • Rosen SW
        • Guyda H
        • Reardon J
        • Scheff M
        The syndrome of basal encephalocele and hypothalamic pituitary dysfunction.
        Annal Int Med. 1978; 89: 910-916